|
KMID : 0388220140210030151
|
|
Journal of the Korean Rheumatism Association
2014 Volume.21 No. 3 p.151 ~ p.155
|
|
|
Coexistence of AA and AL Cardiac Amyloidosis in a Patient with Ankylosing Spondylitis Accompanying Monoclonal Gammopathy of Undetermined Significance
|
|
Kim Woo-Hyeon
Kim Seon-A
Yun Kyung-Jin
Na Soo-Jin
Hyun Ji-In
Jung Jung-Im
Kwok Seung-Ki
Park Sung-Hwan
|
|
|
Abstract
|
|
|
|
Amyloidosis is a clinical disorder caused by extracellular deposition of proteinaceous insoluble fibrils in various tis-sues, resulting in organ compromise. Amyloid L (AL) amy-loidosis is the most common type of systemic amyloidosis, which occurs in association with multiple myeloma or monoclonal gammopathy of undetermined significance (MGUS). Secondary amyloid A (AA) amyloidosis is a com-plication of chronic inflammatory conditions, such as rheu-matoid arthritis or ankylosing spondylitis. We report a case of a 49-year-old manwith a 11-year history of anky-losing spondylitis, who was recently diagnosed with MGUS presented with cardiac amyloidosis of both the AA and AL types. We report this case along with a review of relevant literature.
|
|
|
KEYWORD
|
|
|
Cardiac amyloidosis, Ankylosing spondylitis Monoclonal gammopathy of undetermined significance
|
|
|
FullTexts / Linksout information
|
|
|
|
|
|
Listed journal information
|
|
  
|